Caspian Journal of Pediatrics

en A case report of variant scimitar syndrome تخصصي Special گزارش مورد case report Background: Scimitar syndrome (SS) or congenital pulmonary venolobar syndrome is a rare anomaly, most commonly including partial pulmonary venous drainage into the inferior vena cava, right lung hypoplasia, dextroposition of the heart, and anomalous systemic arterial supply from aorta or one of its branches to the right lung. Case report: A 10-day-old female infant was referred to our hospital with systolic murmur and tachypnea. Initial chest x-ray suggested cardiomegaly and displacement of cardiac structures into the right hemithorax, and initial echocardiogram indicated patent ductus arteriosus, coarctation of aorta, atrial septal defect, ventricular septal defect in this infant who was diagnosed as having SS. Conclusions: We can consider Scimitar syndrome for infants with tachypnea, cyanosis, intrauterine growth restriction (IUGR) and right lobe opacity in chest x-ray. Scimitar Syndrome, Pulmonary venous, Congenital Abnormality, Right lung hypoplasia, Coarctation aorta 253 256 http://caspianjp.ir/browse.php?a_code=A-10-97-1&slc_lang=en&sid=1 Kazem Babazadeh 10031947532846001335 10031947532846001335 No Non-Communicable Pediatric Diseases Research Center, Health Research Institute, Babol University of Medical Sciences, Babol, IR Iran Hassan Zamani 10031947532846001336 10031947532846001336 No Department of Pediatrics, Shahid Modarres Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Hamidreza Ghaemi 10031947532846001337 10031947532846001337 No Non-Communicable Pediatric Diseases Research Center, Health Research Institute, Babol University of Medical Sciences, Babol, IR Iran Forogh Aliakbarnia omran faano60@gmail.com 10031947532846001338 10031947532846001338 Yes Non-Communicable Pediatric Diseases Research Center, Health Research Institute, Babol University of Medical Sciences, Babol, IR Iran